Email this article Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis
- Authors: Soynov I.A.1, Gorbatykh A.V.1, Nichay N.R.1, Omel'chenko A.Y.1, Leykekhman A.V.1, Kulyabin Y.Y.1, Voytov A.V.1, Gorbatykh Y.N.1
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Affiliations:
- Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
- Issue: Vol 45, No 3 (2017)
- Pages: 254-257
- Section: CLINICAL CASES
- URL: https://almclinmed.ru/jour/article/view/547
- DOI: https://doi.org/10.18786/2072-0505-2017-45-3-254-257
- ID: 547
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Abstract
Pulmonary artery agenesis combined with tetralogy of Fallot is the most rarely seen congenital heart disease. Children with this anomaly are an especially problematic category of patients undergoing staged surgical repair. The postoperative period quite often is complicated with shunt thrombosis while a redo open surgery is associated with a very high risk; therefore, endovascular repair is a preferred procedure. We describe a case of right ventricular outflow tract stenting in a 8 month old girl with tetralogy of Fallot and right pulmonary artery agenesis. The patient was admitted at 3 month after performing of a left-sided modified Blalock-Taussig shunt with severe signs of heart failure and desaturation caused by shunt thrombosis. Assessments performed at 2 months after stenting of the outflow tract demonstrated good oxygen saturation in arterial blood (80% and above) and improvement of heart failure symptoms to NYHA II class.
About the authors
I. A. Soynov
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Author for correspondence.
Email: i_soynov@mail.ru
MD, Cardiovascular Surgeon, Congenital Heart Disease Department; Trainee in Research, New Surgical Technologies Center
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation. Tel.: +7 (913) 454 87 52
Russian FederationA. V. Gorbatykh
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Email: fake@neicon.ru
MD, PhD, Cardiovascular Surgeon, Congenital Heart Disease Department; Junior Research Fellow, New Surgical Technologies Center
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation
Russian FederationN. R. Nichay
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Email: fake@neicon.ru
MD, Cardiovascular Surgeon, Congenital Heart Disease Department; Junior Research Fellow, New Surgical Technologies Center
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation
Russian FederationA. Yu. Omel'chenko
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Email: fake@neicon.ru
MD, PhD, Cardiovascular Surgeon, Congenital Heart Disease Department; Senior Research Fellow, New Surgical Technologies Center
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation
Russian FederationA. V. Leykekhman
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Email: fake@neicon.ru
MD, Cardiologist, Congenital Heart Disease Department
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation
Russian FederationYu. Yu. Kulyabin
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Email: fake@neicon.ru
Resident, Congenital Heart Disease Department
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation
Russian FederationA. V. Voytov
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Email: fake@neicon.ru
MD, Cardiovascular Surgeon, Congenital Heart Disease Department
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation
Russian FederationYu. N. Gorbatykh
Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation Pathology
Email: fake@neicon.ru
MD, PhD, Head of Congenital Heart Disease Department
15 Rechkunovskaya ul., Novosibirsk, 630055, Novosibirskaya oblast', Russian Federation
Russian FederationReferences
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